Cystic fibrosis (CF) is a genetic condition that affects multiple organ systems but has greatest impact on the lungs and the digestive system. It is Canada’s most common fatal genetic disease affecting young children and adults. Approximately one in every 3,600 children born in Canada having CF.
Cystic fibrosis does not have a cure but medical advances have radically changed and extended the lives of people with CF. In the 1960’s, the median age of survival for people with CF in Canada was 4 years of age. In 2019, the median age of survival was 57 years and there are now far more adults with CF than children.
The severity of CF differs between individuals. Most CF patients experience persistent and ongoing lung infections which result in progressive destruction and loss of lung function that threaten their lives.
CF is no longer just a childhood disorder. It is very much an expanding complex adult disease with more adult CF patients than pediatric in B.C. We expect the adult CF population to continue growing as management becomes more patient specific.
In partnership with Cystic Fibrosis Canada
and other key stakeholders, CFCBC aims to optimize the delivery of life long, high-quality multidisciplinary patient-centred cystic fibrosis (CF) care that is inclusive, equitable, and accessible province wide while improving the health outcomes of those living with CF.
Several key factors have contributed to the need for a system-based model of care:
- Increasing life expectancy
- Higher patient volumes across B.C.
- Increasing complexity of care and comorbidities requiring frequent access to broader health-care services across the health-care system
- Increasing preventative care to avoid or delay deterioration in lung health
- Increasing hospitalizations as disease severity progresses
- Expensive new therapies aimed at specific gene mutations which require greater CF clinic involvement
- Increasing need for psychosocial support from newborn to end of life
- Improve the health of the CF community
- Reduce the incidence of people experiencing disease through evidence-based clinical prevention strategies
- Enhance primary, community and CF clinic care for patients and families with CF
- Ensure specialized CF care is high quality, evidence based, accessible, and equitable across the province